Coexistent Chiari Malformation and Idiopathic Intracranial Hypertension: Which Should Be Treated First?- Case Report and Review
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چکیده
Previous reports have described concomitant presentation of papilledema and Chiari malformation type 1 (CM1). The pathophysiology of each and their relationship remain poorly understood. As such, different management approaches regarding treating the CM1 or the pseudotumor initially have been described, with varying degrees of success. We report the case of an 11 year old girl with 6 mm tonsillar herniation, a cervicothoracic syrinx, and papilledema who underwent foramen magnum decompression with duraplasty (FMDD). Intracranial pressure (ICP) monitoring revealed elevated ICP before surgery, which resolved postoperatively. The patient had complete resolution of all symptoms and her papilledema and syrinx also resolved.
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تاریخ انتشار 2014